Dermales und subkutanes Leiomyosarkom
Zuletzt aktualisiert: 30.01.2024 | Autor: Doris Helbig
Superfizielle Leiomyosarkome (LMS) sind seltene Tumoren. Diese gehen von Strukturen der Unterhaut (dermales/kutanes Leiomyosarkom) oder des Unterhautfettgewebes (subkutanes LMS) aus (2-3% aller Sarkome) (1-3). Charakteristischerweise sind Personen im Alter von 50-80 Jahren (subkutane LMS tendenziell bei älteren Personen) betroffen (4-8).
Darüber hinaus können primäre superfizielle LMS sehr selten im Rahmen syndromaler Krankheitsbilder auftreten (Reed Syndrom, familiäre/hereditäre Leiomyomatose, Birt-Hogg-Dube Syndrom sowie Li-Fraumeni Syndrom).
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Dermale und subkutane Leiomyosarkome (LMS) sind seltene bösartige Tumoren der Haut.
Sie unterscheiden sich im Wesentlichen durch ihre Entstehung in unterschiedlich tiefen Hautschichten.
- REFERENZEN
- Leitlinienprogramm Onkologie (Deutsche Krebsgesellschaft, Deutsche Krebshilfe, AWMF): S1-Leitlinie Dermales und subkutanes Leiomyosarkom (LMS)
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